PKU is a treatable disease. Treatment involves a diet that is very low in phenylalanine, particularly when the child is growing. The diet must be strictly followed. This requires close supervision by a registered dietitian or doctor, and cooperation of the parent and child. Those who continue the diet into adulthood have better physical and mental health than those who don't stay on it. "Diet for life" has become the standard most experts recommend. It is especially important for women who have PKU to follow the diet before conception and throughout pregnancy.
Carnitine is either obtained from synthesis in the liver, from trimethyl-lysine residues generated during protein catabolism, or from the diet. The main source of carnitine is meat (generally red meats) from cows and pigs and dairy products. Lower amounts are present in beans, nuts,vegetables,fruits,cereals etc. Thus vegetarians may always be at a risk of having lower levels of carnitine in their system. L-carnitine nutritional supplements are thus available for people with deficiency of carnitine . It has been reported that acetyl-L-carnitine nutrional supplements might be better absorbed by the body and therefore have better pharmacological effects as a dietary supplement. 6 L-Carnitine and acetyl-L-carnitine supplements are known to provide cardiovascular and neurological benefits and is believed to help in increasing sperm motility as well.